Dental and Medical Problems

Dent Med Probl
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ISSN 1644-387X (print)
ISSN 2300-9020 (online)
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Dental and Medical Problems

2015, vol. 52, nr 1, January-March, p. 107–111

Publication type: clinical case

Language: English

Creative Commons BY-NC-ND 3.0 Open Access

Second Report of a Mandibular Desmoplastic Fibroma with Sunray Appearance and Review of Other Imaging Features

Drugi opis włókniaka desmoplastycznego dającego odczyn poświaty słonecznej w żuchwie i przegląd innych cech w obrazie radiologicznym

Hamed Jalalian1,A, Hamed Mortazavi2,D,E, Maryam Baharvand2,B

1 Department of Oral and Maxillofacial Surgery, Dental School, Zahedan University of Medical Sciences, Zahedan, Iran

2 Department of Oral and Maxillofacial Medicine, Dental School, Shahid Beheshti University of Medical Sciences, Tehran, Iran


Desmoplastic fibroma (DF) is a rare, non-metastasizing, intraosseous benign but locally aggressive tumor of connective tissue origin, which represents only 0.06% of all bony tumors and 0.3% of benign bony tumors. There are no specific radiological features in the diagnosis of desmoplastic fibroma. Unilocular or multilocular radiolucencies with well-defined borders were generally seen, as well as occasional destruction of the mandibular border and root resorption. One of the extremely rare radiographic patterns in desmoplastic fibroma is a sunray appearance (as a periosteal reaction). According to the data available to us, this radiographic pattern of desmoplastic fibroma was first found by Iwai in a 4-year-old girl. The aim of this article was to present the second report of a pediatric mandibular desmoplastic fibroma with sunray appearance. Meanwhile, a review of literature regarding the different imaging features of desmoplastic fibroma is presented. The key message of this case report is that sunray appearance should be considered a radiographic pattern in benign central tumors such as desmoplastic fibroma by clinicians.

Key words

desmoplastic fibroma, mandible, sunray appearance

Słowa kluczowe

włókniak desmoplastyczny, żuchwa, poświata słoneczna

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